Early adolescent primary ciliary dyskinesia associated with broncholithiasis
S Gundogdu, Koray Hekimoglu
article (Uluslararası, Hakemli) | Yazar(lar): S Gundogdu, Koray Hekimoglu | Yıl: 2008 | Dergi/Kurum: PEDIATRIC PULMONOLOGY | İndeks: WOS.SCI | DOI: 10.1002/ppul.20826 | Anahtar Kelimeler: primary ciliary dyskinesia, Kartagener's syndrome, pulmonary calcification, broncholithiasis, bronchiectasis — Özet: Primary ciliary
Primary ciliary dyskinesia (PCD), is a rare congenital disease group, and contained Kartageners syndrome. This syndrome is characterized with situs viscerum inversus, sinusitis and bronchiectasis. In some elderly patients, broncholithiasis may be associated with PCD. The coexistence of early adolescence PCD and broncolithiasis has not been reported yet. We report here a case of a 14-year-old early adolescent male who had typically presented as PCD-based Kartageners syndrome and developed broncholithiasis which diagnosed with computed tomography.